@prefix p: <http://www.wikidata.org/prop/> .
@prefix rdfs: <http://www.w3.org/2000/01/rdf-schema#> .
@prefix schema1: <http://schema.org/> .
@prefix skos: <http://www.w3.org/2004/02/skos/core#> .
@prefix wd: <http://www.wikidata.org/entity/> .
@prefix wds: <http://www.wikidata.org/entity/statement/> .
@prefix wdt: <http://www.wikidata.org/prop/direct/> .
@prefix wdtn: <http://www.wikidata.org/prop/direct-normalized/> .
@prefix wikibase: <http://wikiba.se/ontology#> .
@prefix xsd: <http://www.w3.org/2001/XMLSchema#> .

wd:Q55950219 rdfs:label "desmoid disease, hereditary"@en,
        "tumeur desmoïde héréditaire"@fr,
        "Doença desmoide"@pt,
        "Doença desmoide"@pt-br ;
    schema1:dateModified "2026-10-24T00:40:15+00:00"^^xsd:dateTime ;
    schema1:description "desmoid tumor (DT) is a benign, locally invasive soft tissue tumor associated with a high recurrence rate but with no metastatic potential"@en ;
    schema1:version 2560167837 ;
    wikibase:identifiers 10,
        12 ;
    wikibase:sitelinks 0 ;
    wikibase:statements 37 ;
    skos:altLabel "Aggressive fibromatosis"@en,
        "DESMOID DISEASE, HEREDITARY"@en,
        "Deep Fibromatosis"@en,
        "Deep Fibromatosis/Desmoid Tumor"@en,
        "Desmoid Fibromatosis"@en,
        "Desmoid Tumor Caused by Somatic Mutation"@en,
        "Desmoid type fibromatosis"@en,
        "Desmoid-Type Fibromatosis"@en,
        "Fibromatosis, Familial Infiltrative"@en,
        "desmoid tumor"@en,
        "hereditary desmoid disease"@en ;
    p:P11430 wds:Q55950219-18c2dcb6-4b9c-1b2c-348a-0e05ec29c32f ;
    p:P11956 wds:Q55950219-619C20D3-5DD2-4306-AEB8-BAC2D33CA003 ;
    p:P14914 wds:Q55950219-9AEC470F-D52F-4F92-9EEB-C3D1A1E2C9E0 ;
    p:P1550 wds:Q55950219-574057B7-6A54-4DCA-89BA-2E58F98B3FAE ;
    p:P1748 wds:Q55950219-3485A680-8C9D-4D44-B230-F3D9239FFCBC ;
    p:P2176 wds:Q55950219-7C26B394-B746-46A3-832D-C8B7915977D4 ;
    p:P2293 wds:Q55950219-CB53017A-A4F3-47C7-919F-5D0F62F4C9E8,
        wds:Q55950219-ECBC4C8E-C782-4D96-986D-2F55F5503C65 ;
    p:P279 wds:Q55950219-4f05d065-444b-b7f0-432d-1f150755fd15,
        wds:Q55950219-75572CA3-269D-48E0-ABB4-731B1F36F895,
        wds:Q55950219-B12F16BB-567C-42DC-BB70-FC1A86483E09 ;
    p:P2841 wds:Q55950219-0889F5D7-BCE4-467A-AB3A-091A6F78125D,
        wds:Q55950219-67B52A8B-3FDD-4B4C-9030-2E0E09BABAD5 ;
    p:P2888 wds:Q55950219-77D83B5B-C090-4EA7-B7C5-B3E2C684F30D,
        wds:Q55950219-C5EF3917-2029-49C3-8FD9-209089B97989,
        wds:Q55950219-D71BF8B7-669E-4C6F-97F5-D69997CADF09 ;
    p:P2892 wds:Q55950219-23F89A00-3437-4CF0-A44A-BE6F1888E84B,
        wds:Q55950219-F17E446A-1D5A-4C40-BDD1-D7BD067DE512,
        wds:Q55950219-F1F97FAE-78F9-4B3F-8B44-662ED653340C ;
    p:P31 wds:Q55950219-42210B16-F875-4239-BE31-02B8C087EE07 ;
    p:P4229 wds:Q55950219-41DE660B-AFA6-4113-A9F3-8A8FEC1E2C00 ;
    p:P492 wds:Q55950219-6380CD25-687D-48CE-BA2F-A18B412B4187 ;
    p:P5270 wds:Q55950219-4E1E0224-2D0C-4393-8148-F1D4F11C2590 ;
    p:P6532 wds:Q55950219-09B50FAA-0AEB-4B0D-A8F4-5F1C27620D48,
        wds:Q55950219-2B642562-6FBE-46D8-A0E4-ED1B7C33912C,
        wds:Q55950219-2FDF42D6-E642-4410-B0FF-3351761284B8,
        wds:Q55950219-58B6136D-2D80-417F-89EE-88B706C3BAE3,
        wds:Q55950219-8E7C5256-21C8-41A1-B5C7-25D990A1C305,
        wds:Q55950219-953CD595-2144-43A7-86CC-D9D19B9079CC,
        wds:Q55950219-9F9059BC-528C-4BA5-9B8E-0E00D2B4486D,
        wds:Q55950219-A2DE77C3-C2CF-42C5-BABF-591AA0BBB36E,
        wds:Q55950219-A9EDAC50-91C5-4781-8D4C-BCAC7BFE98E1,
        wds:Q55950219-CA38C023-794B-4C7F-A472-0F392F5AA3AE,
        wds:Q55950219-D775C71A-3D6B-4554-8E7F-6E7486BCD503,
        wds:Q55950219-EACCD891-31B1-4743-9B21-8D3B443F49E3,
        wds:Q55950219-F014D5D4-70C9-47DD-AB51-FCBFBADEE161 ;
    p:P699 wds:Q55950219-8BB713FC-0B10-400E-8837-42F6885C6082 ;
    wdtn:P5270 <http://purl.obolibrary.org/obo/MONDO_0007608> ;
    wdtn:P699 <http://purl.obolibrary.org/obo/DOID_DOID:0111349> ;
    wdt:P11430 "DI-01711" ;
    wdt:P11956 "0009907" ;
    wdt:P14914 "D00873" ;
    wdt:P1550 "873" ;
    wdt:P1748 "C9182" ;
    wdt:P2176 wd:Q414028 ;
    wdt:P2293 wd:Q14883378,
        wd:Q14902794 ;
    wdt:P279 wd:Q179630,
        wd:Q18553442,
        wd:Q475086 ;
    wdt:P2841 wd:Q21955202,
        wd:Q21955204 ;
    wdt:P2888 <http://identifiers.org/doid/DOID:0111349>,
        <http://purl.obolibrary.org/obo/DOID_0111349>,
        <http://www.orpha.net/ORDO/Orphanet_873> ;
    wdt:P2892 "C0079218",
        "C1851124",
        "C2675440" ;
    wdt:P31 wd:Q112193867 ;
    wdt:P4229 "D48.1" ;
    wdt:P492 "135290" ;
    wdt:P5270 "MONDO_0007608" ;
    wdt:P6532 wd:Q141815351,
        wd:Q1422034,
        wd:Q1442923,
        wd:Q1495657,
        wd:Q16244733,
        wd:Q183134,
        wd:Q183425,
        wd:Q2035084,
        wd:Q4667072,
        wd:Q474959,
        wd:Q683498,
        wd:Q693058,
        wd:Q730877 ;
    wdt:P699 "DOID:0111349" .

