dermatofibrosarcoma protuberans

fibrosarcoma that is located in the dermis layer of the skin
rdfs:label
"dermatofibrosarcoma protuberans"@en
skos:altLabel
"DERMATOFIBROSARCOMA PROTUBERANS"@en
"DERMATOFIBROSARCOMA PROTUBERANS; DFSP"@en
"DFSP"@en
"Dermatofibrosarcoma"@en
"Familial dermatofibrosarcoma protuberans (subtype)"@en
"Giant Cell Fibroblastoma"@en
"Metastatic dermatofibrosarcoma protuberans (subtype)"@en
schema:description
"fibrosarcoma that is located in the dermis layer of the skin"@en
schema:dateModified "2026-10-24T00:03:27+00:00"^^xsd:dateTime
schema:version 2560162045
wikibase:identifiers 31
33
wikibase:sitelinks 10
wikibase:statements 57
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wdt:P10283 "C2778464197"
"C2909576312"
wdt:P11143 "Dermatofibrosarcoma protuberans"
wdt:P1193 0.0003^^xsd:decimal
wdt:P14914 "D31112"
wdt:P1550 "31112"
wdt:P1748 "C4683"
wdt:P18 <http://commons.wikimedia.org/wiki/Special:FilePath/Dermatofibrosarcome%20facial%2001.jpg>
wdt:P1995 oncology
wdt:P2176 imatinib
wdt:P2293 COL1A1
PDGFB
wdt:P279 fibrosarcoma
skin sarcoma
inherited soft tissue tumor
dermis disorder
skin tumor or hamartoma
wdt:P2841 any age
wdt:P2888 <http://identifiers.org/doid/DOID:3507>
<http://purl.obolibrary.org/obo/DOID_3507>
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wdt:P2892 "C0206647"
"C0334464"
"C0392784"
"C3693482"
wdt:P31 type of disease
rare disease
wdt:P3471 "25861"
wdt:P373 "Dermatofibrosarcoma protuberans"
wdt:P4229 "C49.9"
wdt:P4233 "dermatofibrosarcoma-protuberans"
wdt:P4317 "9569"
wdt:P486 "D018223"
wdt:P492 "607907"
wdt:P493 "8832"
wdt:P494 "C49"
wdt:P5008 WikiProject Medicine
wdt:P5270 "MONDO_0011934"
wdt:P557 "31601"
wdt:P563 "8832/3"
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wdt:P6366 "2778464197"
"2909178212"
wdt:P6532 erythema
fibrosarcoma
ulcer
pain
lymphadenopathy
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wdt:P673 "1100203"
wdt:P699 "DOID:3507"
wdt:P7329 "XH9V92"
wdt:P7464 "dermatofibrosarcoma-protuberans"
wdt:P7807 "1980226392"
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