|
rdfs:label
|
"Dermatofibrosarcoma protuberans"@de
"Dermatofibrosarcoma protuberans"@es
"Włókniakomięsak guzowaty skóry"@pl
"dermatofibrosarcoma"@it
"dermatofibrosarcoma protuberans"@cs
"dermatofibrosarcoma protuberans"@en
"dermatofibrosarcoma protuberans"@nn
"dermatofibrosarcoma protuberans"@pt
"dermatofibrosarcoma protuberans"@sl
"dermatofibrosarcome de Darier-Ferrand"@fr
"ساركومة ليفية جلدية حدبية"@ar
"皮肤纤维肉瘤"@zh
"皮膚纖維肉瘤"@zh-hant
"隆起性皮膚線維肉腫"@ja
|
|
skos:altLabel
|
"DERMATOFIBROSARCOMA PROTUBERANS"@en
"DERMATOFIBROSARCOMA PROTUBERANS; DFSP"@en
"DFSP"@en
"DFSP"@fr
"DFSP"@nn
"DFSP"@pl
"DFSP-FS"@fr
"Dermatofibrosarcoma"@en
"Dermatofibrosarcome protubérant"@fr
"Dermofibrosarcoma"@it
"Familial dermatofibrosarcoma protuberans (subtype)"@en
"Giant Cell Fibroblastoma"@en
"Metastatic dermatofibrosarcoma protuberans (subtype)"@en
"dermatofibrosarcoma protuberans )"@pl
"dermatofibrosarkom"@nn
"dermatofibrosarkom protuberans"@nn
|
|
schema:description
|
"Krankheit"@de
"fibrosarcoma that is located in the dermis layer of the skin"@en
"fibrosarcome localisé dans les couches profondes de la peau de type cancéreux"@fr
"fibrosarkom v dermalni plasti (usnjici) kože"@sl
"neoplasia rara di tipo sarcomatoso"@it
"nowotwór człowieka"@pl
"хвороба"@uk
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|
schema:dateModified
|
"2026-10-24T00:03:27+00:00"^^xsd:dateTime
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schema:version
|
2560162045
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|
wikibase:identifiers
|
31
|
|
33
|
|
wikibase:sitelinks
|
10
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|
wikibase:statements
|
57
|
|
p:P10283
|
wd:statement/Q1200239-638DF7FB-8ECE-4A6C-BE16-F06A41DC9EFE
|
|
wd:statement/Q1200239-645A0102-9B09-44F7-9DD1-0D53E8B768B7
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|
p:P11143
|
wd:statement/Q1200239-01CB1BD9-139C-44B8-8625-62BEA4B82482
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|
p:P1193
|
wd:statement/Q1200239-DC25C229-B026-403D-9DB6-816DBB648515
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|
p:P14914
|
wd:statement/Q1200239-6AD083C5-F81D-4314-B9D2-0ACFAA324EF7
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|
p:P1550
|
wd:statement/Q1200239-197E04B8-6D64-4090-BE8A-B24661A5C4D4
|
|
p:P1748
|
wd:statement/Q1200239-a095ff06-4098-71f6-8180-8ab0d00bd120
|
|
p:P18
|
wd:statement/Q1200239-9ebd8e48-454d-648f-44d5-00e4708ca737
|
|
p:P1995
|
wd:statement/Q1200239-1328A997-4671-46E7-9A6F-B40275852DCA
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|
p:P2176
|
wd:statement/Q1200239-160a1798-4e04-6ef7-c957-c2668b699958
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|
p:P2293
|
wd:statement/Q1200239-2FC0576B-0134-49DA-871D-0C08C72BCD7F
|
|
wd:statement/Q1200239-f9c3e20e-4856-c416-f3f8-50d11ab28690
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|
p:P2671
|
wd:statement/Q1200239-5ba2280e-411e-d64e-9179-b735205fcf24
|
|
wd:statement/Q1200239-c602b65e-49e1-9213-761d-19a3f5952779
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|
p:P279
|
wd:statement/Q1200239-22E04CE3-86F4-41B9-AA4D-A128969A600F
|
|
wd:statement/Q1200239-2DD04052-B320-43E2-8B3F-C0B81DF7F921
|
|
wd:statement/Q1200239-5CA30866-FDD8-4B39-AE41-7439D095BFED
|
|
wd:statement/Q1200239-97AA9DE3-49E3-40F4-84D5-E52910671DB4
|
|
wd:statement/Q1200239-CDF5C2E8-90CA-4D05-B40D-3492FF291D57
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|
p:P2841
|
wd:statement/Q1200239-DEDDA896-B184-4969-BB47-88A2B3FA67CF
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|
p:P2888
|
wd:statement/Q1200239-62D7520C-7C89-4CD1-B12C-C141749D3199
|
|
wd:statement/Q1200239-D635EC01-9F23-4115-89A3-AE4637BE3558
|
|
wd:statement/Q1200239-D6EB1AFF-B54E-4D3B-8FCC-9198609104A2
|
|
p:P2892
|
wd:statement/Q1200239-24F8FB56-CEF2-40DC-B98A-E24D3740C373
|
|
wd:statement/Q1200239-758F3D92-89DC-43D0-AAB8-AF303226B96C
|
|
wd:statement/Q1200239-A6423322-84F7-4616-B295-AAA579C3052B
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|
wd:statement/Q1200239-BF833CD0-C914-4638-B0BD-B4C2DD4CC482
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|
p:P31
|
wd:statement/Q1200239-6B3D524A-4672-492F-84B0-FDB67E72A042
|
|
wd:statement/Q1200239-A5B6F53E-595B-4FC1-898F-88954C1C69C5
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|
p:P3471
|
wd:statement/Q1200239-A86DAC84-7885-4188-B94B-BE2254C4C4C5
|
|
p:P373
|
wd:statement/Q1200239-A181F1CD-C7DC-4C82-8AD9-081C9C72C66A
|
|
p:P4229
|
wd:statement/Q1200239-07224238-6D00-40D8-8E53-3B24D9B45E4F
|
|
p:P4233
|
wd:statement/Q1200239-721212f4-4eeb-6ab0-16d8-547c88f3a410
|
|
p:P4317
|
wd:statement/Q1200239-E0F6125E-989C-4782-B827-8505E6E6E414
|
|
p:P486
|
wd:statement/Q1200239-80530C0C-8580-45BA-B109-98A87D636CE0
|
|
p:P492
|
wd:statement/Q1200239-E79BF66E-F8DC-4140-817A-43D7261A9A0D
|
|
p:P493
|
wd:statement/q1200239-2D7C1F00-F79E-4CF1-A95A-619C09CBA88E
|
|
p:P494
|
wd:statement/q1200239-88F2280A-AD9D-49F7-8093-428E3B52ECB4
|
|
p:P5008
|
wd:statement/Q1200239-294D8C71-0ACE-4983-AFD1-0F535DFA1B66
|
|
p:P5270
|
wd:statement/Q1200239-C5815761-51B9-4A64-B499-72485869D366
|
|
p:P557
|
wd:statement/q1200239-B4A48FED-4887-44B4-B680-5DA1E2F16240
|
|
p:P563
|
wd:statement/Q1200239-441969D1-2CBB-4B53-9DC0-FA4DB4226B4B
|
|
wd:statement/q1200239-40B95803-44BB-4BC1-BFBB-E43BD021D9D0
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|
p:P6366
|
wd:statement/Q1200239-4D74C68C-B44B-4A12-B207-57922DEEE244
|
|
wd:statement/Q1200239-E25444C6-A8B7-467C-B653-EDC5FCEBDF5F
|
|
p:P6532
|
wd:statement/Q1200239-071B2F5A-8BE9-46AC-8776-F26D2416493B
|
|
wd:statement/Q1200239-51E1D890-085F-4407-88F0-6EC1F251C95E
|
|
wd:statement/Q1200239-94314F04-6B24-43CB-ADED-45D9C0A7F184
|
|
wd:statement/Q1200239-C4D64B1D-9346-4210-A835-82FFBC5F62E8
|
|
wd:statement/Q1200239-F2575E73-BC88-4266-AC8D-C7CE0D93EA89
|
|
p:P672
|
wd:statement/Q1200239-322F7B1E-1F38-43F4-BB61-4A8764534806
|
|
wd:statement/Q1200239-559DF5B4-70A6-4EFC-8FD0-2337AE82EA1D
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|
p:P673
|
wd:statement/q1200239-BBB4127C-1536-452F-BAF6-156CCF541230
|
|
p:P699
|
wd:statement/Q1200239-5244E217-E51F-4509-89B7-C03312A55223
|
|
p:P7329
|
wd:statement/Q1200239-c7c8f257-c6a8-4818-a158-67241f9a73e8
|
|
p:P7464
|
wd:statement/Q1200239-B73615B4-DCB4-4BE7-8D3D-D9D843AE6B99
|
|
p:P7807
|
wd:statement/Q1200239-311B67AC-2AA8-4CA4-8DE2-DA7674A0050B
|
|
p:direct-normalized/P486
|
<http://id.nlm.nih.gov/mesh/D018223>
|
|
p:direct-normalized/P5270
|
<http://purl.obolibrary.org/obo/MONDO_0011934>
|
|
p:direct-normalized/P6366
|
<https://makg.org/entity/2778464197>
|
|
<https://makg.org/entity/2909178212>
|
|
p:direct-normalized/P672
|
<http://id.nlm.nih.gov/mesh/C04.557.450.565.590.350.320>
|
|
<http://id.nlm.nih.gov/mesh/C04.557.450.795.350.320>
|
|
p:direct-normalized/P699
|
<http://purl.obolibrary.org/obo/DOID_DOID:3507>
|
|
wdt:P10283
|
"C2778464197"
|
|
"C2909576312"
|
|
wdt:P11143
|
"Dermatofibrosarcoma protuberans"
|
|
wdt:P1193
|
0.0003^^xsd:decimal
|
|
wdt:P14914
|
"D31112"
|
|
wdt:P1550
|
"31112"
|
|
wdt:P1748
|
"C4683"
|
|
wdt:P18
|
<http://commons.wikimedia.org/wiki/Special:FilePath/Dermatofibrosarcome%20facial%2001.jpg>
|
|
wdt:P1995
|
oncology
|
|
wdt:P2176
|
imatinib
|
|
wdt:P2293
|
COL1A1
|
|
PDGFB
|
|
wdt:P279
|
fibrosarcoma
|
|
skin sarcoma
|
|
inherited soft tissue tumor
|
|
dermis disorder
|
|
skin tumor or hamartoma
|
|
wdt:P2841
|
any age
|
|
wdt:P2888
|
<http://identifiers.org/doid/DOID:3507>
|
|
<http://purl.obolibrary.org/obo/DOID_3507>
|
|
<http://www.orpha.net/ORDO/Orphanet_31112>
|
|
wdt:P2892
|
"C0206647"
|
|
"C0334464"
|
|
"C0392784"
|
|
"C3693482"
|
|
wdt:P31
|
type of disease
|
|
rare disease
|
|
wdt:P3471
|
"25861"
|
|
wdt:P373
|
"Dermatofibrosarcoma protuberans"
|
|
wdt:P4229
|
"C49.9"
|
|
wdt:P4233
|
"dermatofibrosarcoma-protuberans"
|
|
wdt:P4317
|
"9569"
|
|
wdt:P486
|
"D018223"
|
|
wdt:P492
|
"607907"
|
|
wdt:P493
|
"8832"
|
|
wdt:P494
|
"C49"
|
|
wdt:P5008
|
WikiProject Medicine
|
|
wdt:P5270
|
"MONDO_0011934"
|
|
wdt:P557
|
"31601"
|
|
wdt:P563
|
"8832/3"
|
|
"8833/3"
|
|
wdt:P6366
|
"2778464197"
|
|
"2909178212"
|
|
wdt:P6532
|
erythema
|
|
fibrosarcoma
|
|
ulcer
|
|
pain
|
|
lymphadenopathy
|
|
wdt:P672
|
"C04.557.450.565.590.350.320"
|
|
"C04.557.450.795.350.320"
|
|
wdt:P673
|
"1100203"
|
|
wdt:P699
|
"DOID:3507"
|
|
wdt:P7329
|
"XH9V92"
|
|
wdt:P7464
|
"dermatofibrosarcoma-protuberans"
|
|
wdt:P7807
|
"1980226392"
|