microscopic polyangiitis

inflammatory, necrotizing, systemic vasculitis that affects predominantly small vessels in multiple organs
rdfs:label
"microscopic polyangiitis"@en
skos:altLabel
"MPA"@en
"Micropolyangiitis"@en
"Microscopic polyarteritis"@en
schema:description
"inflammatory, necrotizing, systemic vasculitis that affects predominantly small vessels in multiple organs"@en
schema:dateModified "2026-10-24T00:32:48+00:00"^^xsd:dateTime
schema:version 2560166744
wikibase:identifiers 27
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p:direct-normalized/P3201 <http://purl.bioontology.org/ontology/MDRFRE/10063344>
p:direct-normalized/P486 <http://id.nlm.nih.gov/mesh/D055953>
p:direct-normalized/P5270 <http://purl.obolibrary.org/obo/MONDO_0019124>
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<http://id.nlm.nih.gov/mesh/C14.907.253.329.600>
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<http://id.nlm.nih.gov/mesh/C17.800.862.105.750>
<http://id.nlm.nih.gov/mesh/C20.111.193.750>
wdt:P10283 "C2778910314"
wdt:P11143 "Microscopic polyangiitis"
wdt:P1193 0.00005^^xsd:decimal
wdt:P11956 "1000784"
wdt:P1325 <http://www.nanbyou.or.jp/entry/86>
wdt:P14914 "D00727"
wdt:P1550 "727"
wdt:P1748 "C70549"
wdt:P1814 "けんびきょうてきたはつけっかんえん"
wdt:P1995 immunology
rheumatology
wdt:P2176 rituximab
wdt:P279 anti-neutrophil cytoplasmic antibody-associated vasculitis
peripheral vascular disease
systemic inflammatory disease associated with an acquired peripheral neuropathy
secondary glomerular disease
wdt:P2841 childhood onset
adult onset
wdt:P2888 <http://www.orpha.net/ORDO/Orphanet_727>
wdt:P2892 "C0343192"
"C2347126"
wdt:P31 type of disease
designated intractable/rare disease
wdt:P3201 "10063344"
wdt:P4229 "M31.7"
wdt:P4233 "microscopic-polyangiitis"
wdt:P4317 "3652"
wdt:P486 "D055953"
wdt:P493 "446.0"
wdt:P494 "M31.7"
wdt:P5270 "MONDO_0019124"
wdt:P557 "8193"
wdt:P604 "000874"
wdt:P6366 "2778910314"
wdt:P646 "/m/071ppt"
wdt:P6532 joint inflammation
erythema
Subcutaneous hemorrhage
Nausea and vomiting
Abnormal retinal vascular morphology
Palpable purpura
gastrointestinal bleeding
pancreatitis
gangrene
abdominal pain
nosebleed
peritonitis
cutis marmorata
hematuria
myalgia
kidney failure
pericarditis
anemia
glomerulonephritis
vasculitis
ulcer
chest pain
weight loss
retinal vasculitis
fatigue
wdt:P665 "H01658"
wdt:P672 "C10.228.140.300.275.600"
"C14.907.253.329.600"
"C14.907.940.897.249.500"
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wdt:P673 "334024"
wdt:P7329 "4A44.A0"
wdt:P7807 "999231798"
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