idiopathic pulmonary fibrosis

chronic, irreversible and ultimately fatal disease characterized by a progressive decline in lung function
rdfs:label
"idiopathic pulmonary fibrosis"@en
skos:altLabel
"FIBROCYSTIC PULMONARY DYSPLASIA"@en
"IDIOPATHIC PULMONARY FIBROSIS, FAMILIAL"@en
"IPF"@en
"cryptogenic fibrosing alveolitis"@en
schema:description
"chronic, irreversible and ultimately fatal disease characterized by a progressive decline in lung function"@en
schema:dateModified "2026-10-23T23:36:00+00:00"^^xsd:dateTime
schema:version 2560156452
wikibase:identifiers 32
37
wikibase:sitelinks 29
wikibase:statements 79
p:P10283 wd:statement/Q2290446-5F66813C-9225-4D53-9674-32028905AE6B
p:P10565 wd:statement/Q2290446-E728A30C-D04E-43C0-B2F4-78F4E80DD28B
p:P11143 wd:statement/Q2290446-8EC709D6-997D-48E7-9CD3-465A2EBDBC4B
p:P11430 wd:statement/Q2290446-7496ca55-4438-0d70-6543-8e10714d7218
p:P1193 wd:statement/Q2290446-6E597E4C-4864-45A2-82A9-A9ECB74C7038
p:P13204 wd:statement/Q2290446-9FF49C56-68D4-4969-A1B7-65BD582465D9
p:P1417 wd:statement/Q2290446-1D1B6FEB-8269-4981-BC7E-4944EFE97538
p:P14541 wd:statement/Q2290446-E7F774D9-EBF3-4FE2-A5A3-5955912E5497
p:P1461 wd:statement/Q2290446-770FCA06-D793-455F-B191-10F069AC1F02
p:P14914 wd:statement/Q2290446-31D3B0CF-10B8-43C4-97F0-2086BB8F4459
p:P1550 wd:statement/Q2290446-e30311b4-4278-43d4-4241-bc4a618b0b6d
p:P1692 wd:statement/Q2290446-40C713A9-C905-4016-AFF3-F8E385F42E90
p:P1748 wd:statement/Q2290446-BAB0906E-0AA9-478D-89BC-CBFE389EC294
wd:statement/Q2290446-D16C3C10-DC50-4032-BBBC-1B201E36D5FE
p:P18 wd:statement/Q2290446-99729DE2-39AB-48D1-9578-A6D8AF1240A0
p:P1995 wd:statement/Q2290446-5D9375D1-4BAF-46A8-A188-E9233062A8E2
p:P2293 wd:statement/Q2290446-0C4BAADA-F630-4E07-826B-8A99C817326F
wd:statement/Q2290446-193B369F-0875-4614-8E9A-0AD14AFE01A8
wd:statement/Q2290446-2A2CEB97-C41B-4F41-8925-036163ABAA0F
wd:statement/Q2290446-380E9CBA-536B-4536-A43B-C068DC85B866
wd:statement/Q2290446-3AFEC731-5A8D-46F6-9342-1DB12610FC1B
wd:statement/Q2290446-42D1BF5A-049D-4986-B282-937E2DCE0147
wd:statement/Q2290446-5111886B-0EEE-4A5F-A2BA-AC9BE6B42871
wd:statement/Q2290446-51810A1D-4717-47F5-B353-3F8F1FD98246
wd:statement/Q2290446-587F8DE5-989C-453F-9645-D71676ACE2BE
wd:statement/Q2290446-692F2747-E01B-48C0-BA66-5B28131F3268
wd:statement/Q2290446-A393E704-43CA-4DE8-8F9A-1060799FB363
wd:statement/Q2290446-BCC105D2-E681-42FA-A07E-B0853B8D3F1F
wd:statement/Q2290446-D0FDC1EA-8909-4077-9933-1081EEF2BA86
wd:statement/Q2290446-D10DC543-F0F8-4DF5-BC39-BDE42DFA53FC
wd:statement/Q2290446-D5693D20-547C-4C5C-A6B2-37D31CC5166A
p:P279 wd:statement/Q2290446-4627D4AC-34E1-470F-AF9E-509D038C2C63
wd:statement/Q2290446-f8d4f2fd-4193-c1df-d082-f363f9e0a3f0
p:P2841 wd:statement/Q2290446-323F8EE0-DE9C-4095-8CFB-20C4C63C8D19
p:P2888 wd:statement/Q2290446-A5360B82-B79E-4A4B-A858-8600D6770DF9
wd:statement/Q2290446-C4CD32A1-15F6-475D-AB0C-5B244A3927EF
p:P2892 wd:statement/Q2290446-9130C8BA-0813-4CAC-AEC3-0E9DCF563EC9
p:P31 wd:statement/Q2290446-3481EECD-1542-48C8-B6DF-8EB70B095A4F
p:P373 wd:statement/Q2290446-cda118c2-4a48-b3f6-fa93-052ffe4c9e69
p:P3827 wd:statement/Q2290446-80BD2180-9394-46B6-AE48-275E106F806F
p:P3841 wd:statement/Q2290446-2B08892F-677B-483E-A804-77C4DDF485A5
p:P3984 wd:statement/Q2290446-38531ddb-4f4b-38bd-6090-309947f4604c
p:P4229 wd:statement/Q2290446-142A4F97-0330-4317-A269-E48387B77771
p:P4317 wd:statement/Q2290446-FF920F9B-6882-43A0-80AA-047F82181FED
p:P4342 wd:statement/Q2290446-c1c78c1f-40e0-f2c8-79c1-a32d86a85a19
p:P4527 wd:statement/Q2290446-DDAC4369-6826-42C0-9A44-D40AA04E738A
p:P486 wd:statement/Q2290446-9A734805-1C86-498D-A0CD-465A3813C33E
p:P492 wd:statement/q2290446-7D8E6588-37F5-410B-BF81-6479A182689B
p:P5008 wd:statement/Q2290446-405A9D32-F3C8-46ED-9472-49FB8C07FB7E
p:P557 wd:statement/q2290446-CC8BFFC2-9BA4-4CC1-A5E7-FFF48B0B2D8B
p:P5806 wd:statement/Q2290446-53e91d72-4922-2d3c-0550-5ed1f2c9aad8
p:P604 wd:statement/q2290446-C707DCD3-58D9-4A21-A3A3-97CC1759DBA5
p:P6366 wd:statement/Q2290446-2662E6BF-2B0B-41C9-A1A8-C38373D62F50
p:P646 wd:statement/Q2290446-2588A589-D9AF-4E4E-8BB4-FBF40723BDB6
p:P6532 wd:statement/Q2290446-0B35A6CC-A303-4487-B516-A8799CB45D6B
wd:statement/Q2290446-10F83F2B-7F2B-49C3-80BC-DB76872D9223
wd:statement/Q2290446-123248D7-3747-4C6D-A13D-0E328AF3D165
wd:statement/Q2290446-2089EF5A-CE76-4362-997A-2A607F8878AC
wd:statement/Q2290446-2319E0AA-B9F4-4488-8A7F-8FE4178B283A
wd:statement/Q2290446-319A530B-A5CE-4CF3-A61F-65F9273A2A24
wd:statement/Q2290446-33FF71F3-5DCC-487A-BE56-E9C8164AB76D
wd:statement/Q2290446-42DCB15D-5CAE-4CCB-8116-FDC4C0343F36
wd:statement/Q2290446-595AC012-EAD1-47EF-9B12-38301FCA076C
wd:statement/Q2290446-71F34C48-0E76-4882-8FF4-5C4B02966F13
wd:statement/Q2290446-728FEADD-F863-48D8-9B10-7D01DEDD2127
wd:statement/Q2290446-98715B67-346F-406F-BE70-812421796732
wd:statement/Q2290446-B49B11A9-4B8C-4088-9564-2428D48501B5
wd:statement/Q2290446-F25BDFC2-4A13-4E36-8AFD-B3A2226EDB14
p:P665 wd:statement/Q2290446-BAB50D32-718A-48B0-86DB-2D4DB7571734
p:P668 wd:statement/Q2290446-47b65c47-4910-c48d-dc58-293a1570c75f
p:P672 wd:statement/Q2290446-4C6EA7F1-EF42-44F2-B04E-6B0AD70609AE
p:P673 wd:statement/Q2290446-F433A530-8043-4941-A39C-0667DDD0F248
wd:statement/q2290446-C7ECBFDA-4B91-4A59-BD0D-A80719FCBAF4
p:P699 wd:statement/Q2290446-8D67D3AE-A99D-4ECB-988C-FF70E22994EA
p:P7329 wd:statement/Q2290446-54C62C93-F943-4AB7-A984-B5BE9E6FB53D
p:P7464 wd:statement/Q2290446-BC9D8A49-D71B-466A-9166-63843181E132
p:P7807 wd:statement/Q2290446-E1DD3BAF-743E-443A-9F49-708585AEDADB
p:P8687 wd:statement/Q2290446-53ef2c1b-45f6-490a-f12c-d2c1cf3b144d
p:P9272 wd:statement/Q2290446-CC3ACBE8-CF65-4705-84B4-3EEB75B6C58A
p:direct-normalized/P4527 <http://data.parliament.uk/terms/423326>
p:direct-normalized/P486 <http://id.nlm.nih.gov/mesh/D054990>
p:direct-normalized/P5806 <http://snomed.info/id/700250006>
p:direct-normalized/P6366 <https://makg.org/entity/2778341716>
p:direct-normalized/P665 <http://www.kegg.jp/entry/H01299>
p:direct-normalized/P672 <http://id.nlm.nih.gov/mesh/C08.381.483.652.500>
p:direct-normalized/P699 <http://purl.obolibrary.org/obo/DOID_DOID:0050156>
wdt:P10283 "C2778341716"
wdt:P10565 "448086"
wdt:P11143 "Idiopathic pulmonary fibrosis"
wdt:P11430 "DI-02670"
wdt:P1193 0.0003^^xsd:decimal
wdt:P13204 "vhyzue45"
wdt:P1417 "topic/idiopathic-pulmonary-fibrosis"
wdt:P14541 "1pJqEy"
wdt:P1461 "idiopathic-pulmonary-fibrosis"
wdt:P14914 "D02032"
wdt:P1550 "2032"
wdt:P1692 "516.31"
wdt:P1748 "C35715"
"C35716"
wdt:P18 <http://commons.wikimedia.org/wiki/Special:FilePath/Ipf%20NIH.jpg>
wdt:P1995 pulmonology
wdt:P2293 DSP
TERT
PARN
TERC
FAM13A
ATP11A
RTEL1
STN1
DPP9
MDGA2
SFTPA1
MUC5B
SFTPA2
ABCA3
SFTPC
wdt:P279 idiopathic interstitial pneumonia
pulmonary fibrosis
wdt:P2841 adult onset
wdt:P2888 <http://identifiers.org/doid/DOID:0050156>
<http://purl.obolibrary.org/obo/DOID_0050156>
wdt:P2892 "C1800706"
wdt:P31 type of disease
wdt:P373 "Idiopathic pulmonary fibrosis"
wdt:P3827 "idiopathic-pulmonary-fibrosis"
wdt:P3841 "HP:0031950"
wdt:P3984 "pulmonaryfibrosis"
wdt:P4229 "J84.112"
wdt:P4317 "8609"
wdt:P4342 "idiopatisk_pulmonal_fibrose"
wdt:P4527 "423326"
wdt:P486 "D054990"
wdt:P492 "178500"
wdt:P5008 WikiProject Medicine
wdt:P557 "4815"
wdt:P5806 "700250006"
wdt:P604 "000069"
wdt:P6366 "2778341716"
wdt:P646 "/m/02pfs8g"
wdt:P6532 interstitial lung disease
Honeycomb lung
secondary hypertrophic osteoarthropathy
acrocyanosis
orthodeoxia
dyspnea on effort
idiopathic pulmonary fibrosis
pulmonary fibrosis
bronchiectasis
cough
pulmonary valve insufficiency
pulmonary adventitious sound
exercise intolerance
fatigue
wdt:P665 "H01299"
wdt:P668 "NBK1230"
wdt:P672 "C08.381.483.652.500"
wdt:P673 "301226"
"363273"
wdt:P699 "DOID:0050156"
wdt:P7329 "CB03.4"
wdt:P7464 "idiopathic-pulmonary-fibrosis"
wdt:P7807 "1074069640"
wdt:P8687 941.0^^xsd:decimal
wdt:P9272 "53083"
Download as:
TurtleJSON-LDRDF/XML
data from SPARQL profile: Wikidata