Churg-Strauss syndrome

a systemic vasculitis realized as blood vessel inflammation, with symptoms asthma along with hay fever, rash and gastrointestinal bleeding
rdfs:label
"Churg-Strauss syndrome"@en
skos:altLabel
"Allergic Angiitides"@en
"Allergic Angiitides, Granulomatous"@en
"Allergic Angiitis"@en
"Allergic Angiitis and Granulomatosis"@en
"Allergic Angiitis, Granulomatous"@en
"Allergic Granulomatoses"@en
"Allergic Granulomatosis"@en
"Allergic Granulomatous Angiitides"@en
"Allergic Granulomatous Angiitis"@en
"Allergic Granulomatous and Angiitis"@en
"Allergic granulomatosis angiitis"@en
"Allergic granulomatosis angiitis (disorder)"@en
"Angiitides, Allergic"@en
"Angiitides, Allergic Granulomatous"@en
"Angiitides, Granulomatous Allergic"@en
"Angiitis, Allergic"@en
"Angiitis, Allergic Granulomatous"@en
"Angiitis, Granulomatous Allergic"@en
"Churg Strauss Syndrome"@en
"Churg-Strauss Syndrome"@en
"Churg-Strauss vasculitis"@en
"Churg–Strauss syndrome"@en
"EGPA"@en
"Eosinophilic Granulomatous Vasculitides"@en
"Eosinophilic Granulomatous Vasculitis"@en
"Eosinophilic granulomatosis with Polyangitis"@en
"Eosinophilic granulomatosis with polyangiitis"@en
"Eosinophilic multiple vasculitis granulomatous disease"@en
"Granulomatoses, Allergic"@en
"Granulomatosis, Allergic"@en
"Granulomatous Allergic Angiitides"@en
"Granulomatous Angiitides, Allergic"@en
"Granulomatous Angiitis, Allergic"@en
"Granulomatous Vasculitides, Eosinophilic"@en
"Granulomatous Vasculitis, Eosinophilic"@en
"Granulomatous allergic angiitis"@en
"Syndrome, Churg-Strauss"@en
"Vasculitides, Eosinophilic Granulomatous"@en
"Vasculitis, Churg Strauss"@en
"Vasculitis, Churg-Strauss"@en
"Vasculitis, Eosinophilic Granulomatous"@en
schema:description
"a systemic vasculitis realized as blood vessel inflammation, with symptoms asthma along with hay fever, rash and gastrointestinal bleeding"@en
schema:dateModified "2026-10-23T23:33:25+00:00"^^xsd:dateTime
schema:version 2560155986
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<http://id.nlm.nih.gov/mesh/C15.604.515.292.015>
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<http://id.nlm.nih.gov/mesh/C20.111.193.500>
p:direct-normalized/P699 <http://purl.obolibrary.org/obo/DOID_DOID:3049>
wdt:P10283 "C2776263479"
wdt:P11143 "Eosinophilic granulomatosis with polyangiitis"
wdt:P1193 0.00005^^xsd:decimal
wdt:P11956 "0007208"
wdt:P1325 <http://www.nanbyou.or.jp/entry/3877>
wdt:P138 Jacob Churg
Lotte Strauss
wdt:P1461 "churg-strauss-syndrome"
wdt:P14914 "D00183"
wdt:P1550 "183"
wdt:P1748 "C34481"
wdt:P18 <http://commons.wikimedia.org/wiki/Special:FilePath/Churg-Strauss%20syndrome%20-%20high%20mag.jpg>
<http://commons.wikimedia.org/wiki/Special:FilePath/Churg-Strauss%20syndrome%20-%20very%20high%20mag.jpg>
wdt:P1995 immunology
rheumatology
wdt:P2176 mepolizumab
wdt:P227 "4302465-8"
wdt:P244 "sh96009247"
wdt:P279 anti-neutrophil cytoplasmic antibody-associated vasculitis
systemic inflammatory disease associated with an acquired peripheral neuropathy
non-familial rare disease with dilated cardiomyopathy
secondary glomerular disease
wdt:P2841 juvenile onset
adult onset
late onset
wdt:P2888 <http://identifiers.org/doid/DOID:3049>
<http://purl.obolibrary.org/obo/DOID_3049>
<http://www.orpha.net/ORDO/Orphanet_183>
wdt:P2892 "C0008728"
wdt:P31 type of disease
designated intractable/rare disease
wdt:P3471 "39230"
wdt:P3720 "13631492"
wdt:P373 "Churg-Strauss syndrome"
wdt:P4229 "M30.1"
wdt:P4233 "churg-strauss-syndrome"
wdt:P4317 "6111"
wdt:P486 "D015267"
wdt:P493 "447.6"
wdt:P5008 WikiProject Medicine
wdt:P5270 "MONDO_0015943"
wdt:P557 "2685"
wdt:P646 "/m/03y08x"
wdt:P6532 myocardial infarction
Hypopigmented skin patches
Abnormal pericardium morphology
Nausea and vomiting
Increased circulating IgE concentration
pulmonary infiltrate
cranial nerve palsy
myocarditis
acrocyanosis
eosinophilic gastroenteritis
cutis marmorata
glomerulopathy
asthma
fever
myalgia
kidney failure
eosinophilia
transient cerebral isolation
endocarditis
gait abnormality
peripheral neuropathy
fatigue
wdt:P665 "H01468"
wdt:P672 "C14.907.940.897.249.249"
"C15.604.515.292.015"
"C17.800.862.105.500"
"C20.111.193.500"
wdt:P673 "1083013"
"1178795"
wdt:P699 "DOID:3049"
wdt:P7329 "4A44.A2"
wdt:P780 gastrointestinal bleeding
bleeding
wdt:P7807 "835880885"
wdt:P8189 "987007566180005171"
wdt:P8313 "eosinofil_granulomatøs_polyangiitis_(EGPA)"
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