frataxin

mammalian protein found in Homo sapiens
rdfs:label
"frataxin"@en
skos:altLabel
"FXN"@en
"Friedreich ataxia protein"@en
"frataxin, mitochondrial"@en
schema:description
"mammalian protein found in Homo sapiens"@en
schema:dateModified "2026-07-23T06:51:11+00:00"^^xsd:dateTime
schema:version 2521519672
wikibase:identifiers 25
wikibase:sitelinks 11
wikibase:statements 86
p:P10283 wd:statement/Q409999-D476F0D0-39B1-4E33-823F-6C58BD198F01
p:P2888 wd:statement/Q409999-1B6DAA78-4D41-4D91-80AD-FED1DFC9A266
p:P31 wd:statement/Q409999-211BC58A-132D-4888-8537-9DD77C2EDB2B
p:P3417 wd:statement/Q409999-669243F2-9061-4C02-A63E-76E6695D5C47
p:P352 wd:statement/Q409999-82872CD5-7EA6-4065-A861-64449718D50A
p:P361 wd:statement/Q409999-0EE827D1-14DA-4204-8876-4F43B39BEA20
wd:statement/Q409999-225557BF-A880-42C1-9C33-6C5A72B7AA2A
wd:statement/Q409999-68CA50AB-B18C-4ABE-9C75-0802BD7935B9
wd:statement/Q409999-F905E288-BB6E-4F2A-B222-748DCEF72BC2
p:P373 wd:statement/Q409999-b11b708e-23b5-45c7-916f-0e628993c109
p:P527 wd:statement/Q409999-BC11A0EE-6E2D-49DF-976F-B909D3DF76EC
p:P591 wd:statement/Q409999-A8941F7D-0124-4E4E-A9B6-DF7092E42871
p:P6366 wd:statement/Q409999-3C8EA171-229A-41DD-B4F7-C777AA69C31A
p:P637 wd:statement/Q409999-C9013A6D-121B-4035-93B2-AA6124F17F75
wd:statement/Q409999-E9D4B13F-3065-4B69-AFF1-435A54B9A236
p:P638 wd:statement/Q409999-0394FB39-8137-4CDE-AA58-91603D8CE1A7
wd:statement/Q409999-0548E531-25E6-41DB-B3C1-1418645C4BC1
wd:statement/Q409999-38AD88C1-8872-4377-9D92-88847176301C
wd:statement/Q409999-4136FD21-3031-41CC-82D5-35A5E2748535
wd:statement/Q409999-782F9DCE-718C-480C-9D47-ECD907F55434
wd:statement/Q409999-867A2BA6-11CA-4EAB-9531-54702FF4DFF4
wd:statement/Q409999-87862BC7-15A4-4DD6-9184-2FE8A0F9C3B4
wd:statement/Q409999-957A6E4E-DBED-472B-A97C-E15BF36A6150
wd:statement/Q409999-D4ABCF3A-AA6B-441A-B1C1-AEDCDD24BA13
wd:statement/Q409999-E7ED8AAE-A958-4640-8395-7BB1ADB52672
wd:statement/Q409999-E9E1E4C3-8054-441F-8970-C2BCEE82D46A
p:P646 wd:statement/Q409999-C31F41C6-E9AF-4017-A2FA-5775FE94FC72
p:P680 wd:statement/Q409999-02E5275E-8AC9-48CD-96C0-C5EC29F58A16
wd:statement/Q409999-0C08FD56-9D4B-491B-A3FB-F6396730866B
wd:statement/Q409999-114F810A-F8E4-4222-B99F-AF890C81FC67
wd:statement/Q409999-1F92AE5E-E737-443A-BCFA-67977744B504
wd:statement/Q409999-2DE1C33E-F776-4A06-85BC-909B70097BA0
wd:statement/Q409999-345C6706-B55D-4742-BCC2-AE97F91AB6F2
wd:statement/Q409999-52D10533-237E-428E-B2E3-EA6FE5AE18E7
wd:statement/Q409999-9B9B50C7-65A4-4559-8DF9-90EEFA2FE286
wd:statement/Q409999-9DFC55D6-05B3-421B-B9DE-87BEA2BBB50B
wd:statement/Q409999-A39A76BB-8446-4355-99DA-8971BAF50BFB
wd:statement/Q409999-A90A07E0-1AFB-4B5A-B4C4-3A53B6E3D298
wd:statement/Q409999-AF672BFC-60BF-4526-88F2-2F8A308CA5CF
wd:statement/Q409999-DBF4DB2C-4747-4862-A783-D9953FF8F61C
p:P681 wd:statement/Q409999-4D8B6459-D5C7-4228-AA3E-717D006FDE4A
wd:statement/Q409999-5F653DA3-1F0A-476B-9667-32BD4BDFFBE1
wd:statement/Q409999-6CB7E498-7031-40F1-88FD-6778D8D7E094
wd:statement/Q409999-ADFBC8DA-E485-426E-9D99-E391E23EDFE8
wd:statement/Q409999-D0ADD0F7-E8BC-4598-8DC9-F8D72CAB24C6
wd:statement/Q409999-DE3C1E38-CEF8-46F0-B150-4795676AAF32
p:P682 wd:statement/Q409999-02A0D20F-C8FB-4FAD-BEAE-66E78CBE9686
wd:statement/Q409999-0B0EEAF8-650B-4A92-B5B6-1F6439C05383
wd:statement/Q409999-0D52254E-9A39-4C8C-B49F-94E31866A27E
wd:statement/Q409999-15963A63-7ED0-4811-B17F-FCF328FEF2DB
wd:statement/Q409999-1D723E18-B3FA-4783-B030-C11DDFBB2720
wd:statement/Q409999-1E9D5607-A014-41AF-8806-D602BE2C15C5
wd:statement/Q409999-221B1C81-2A28-4A51-9FC1-2F65CD0FDF33
wd:statement/Q409999-2A000144-E8D2-41B2-82DF-7B4C94549FEE
wd:statement/Q409999-33261792-6D58-45EC-AAFF-E4D9A3A8B96B
wd:statement/Q409999-354F80B8-4522-4C43-A30C-978EE299C6E6
wd:statement/Q409999-3942D30A-EACC-42D9-8BC9-F9A936E0A5DE
wd:statement/Q409999-3E16A7FF-FFB6-4A32-89D5-B2EEEECA8527
wd:statement/Q409999-47524869-AB14-437C-91DD-36FBCB207F4A
wd:statement/Q409999-4A0C7BDD-620E-4E1A-A327-90836F844263
wd:statement/Q409999-50FFDE05-1C58-47E9-87EE-DA993911BB7C
wd:statement/Q409999-53EA19B3-D7F4-482B-88B2-8C96ED13111A
wd:statement/Q409999-559F9D25-5A9A-4B53-AFF9-5FDB20ECA8EA
wd:statement/Q409999-7CCF5B7B-4F99-4597-8509-487C19BF3555
wd:statement/Q409999-7CE1AFA3-1C5F-41F7-B5B7-069506FA58F6
wd:statement/Q409999-7DE3E6FF-4A1F-4F34-9717-7A13187D92D7
wd:statement/Q409999-88B92689-07F5-4551-A79C-0DC03CD022B6
wd:statement/Q409999-958760B3-4D87-426D-B4CA-F0979508DB8B
wd:statement/Q409999-A746E7B8-6B7F-406E-B6CE-97FC83981381
wd:statement/Q409999-AAF3A9E4-D3D5-4DAA-B56D-C33986249C8A
wd:statement/Q409999-BE413942-BCE2-47B5-AD72-84E1D4EB644D
wd:statement/Q409999-C1EF0BFB-3697-4754-80BE-896A17AEA7D8
wd:statement/Q409999-CD72B24E-8CF3-44E4-8C69-295719A3CCA7
wd:statement/Q409999-D7BB0E4D-FEEB-4084-905A-702ADE09A088
wd:statement/Q409999-F2FD6C0C-C201-438E-8D66-DE2DE032170E
wd:statement/Q409999-FA1F44BC-4B70-4FDA-81E3-C8B8F52B13F7
p:P692 wd:statement/Q409999-33EC1240-0481-46AD-BDF9-1BFEEFCA5CA7
p:P702 wd:statement/Q409999-07827540-5EAF-4448-8C68-2A0FDBE51932
p:P703 wd:statement/Q409999-ED6A1E96-C76D-4B54-93C8-E2339B8E0A79
p:P705 wd:statement/Q409999-14B06224-34B3-45DB-AF41-04ECE43507E8
wd:statement/Q409999-4664E74C-0117-4215-8523-B7CDC331C2C5
wd:statement/Q409999-5F8F5AC3-1DD5-4AC9-8FE1-43CB2C4ADA63
wd:statement/Q409999-8C33901B-F00E-4D4D-B18F-D80ECDD2C112
wd:statement/Q409999-91B456A1-A1E7-4EF3-B528-888270E297B8
wd:statement/Q409999-BD9350D3-E2C7-4E07-8940-D5CD0B639C6F
p:P7260 wd:statement/Q409999-4E1EA1F2-CC04-4C04-BE9F-20028DE0D403
p:direct-normalized/P352 <http://purl.uniprot.org/uniprot/Q16595>
p:direct-normalized/P6366 <https://makg.org/entity/2779314966>
p:direct-normalized/P637 <http://purl.uniprot.org/refseq/NP_000135>
<http://purl.uniprot.org/refseq/NP_852090>
p:direct-normalized/P638 <https://rdf.wwpdb.org/pdb/1EKG>
<https://rdf.wwpdb.org/pdb/1LY7>
<https://rdf.wwpdb.org/pdb/3S4M>
<https://rdf.wwpdb.org/pdb/3S5D>
<https://rdf.wwpdb.org/pdb/3S5E>
<https://rdf.wwpdb.org/pdb/3S5F>
<https://rdf.wwpdb.org/pdb/3T3J>
<https://rdf.wwpdb.org/pdb/3T3K>
<https://rdf.wwpdb.org/pdb/3T3L>
<https://rdf.wwpdb.org/pdb/3T3T>
<https://rdf.wwpdb.org/pdb/3T3X>
wdt:P10283 "C2779314966"
wdt:P2888 <http://purl.uniprot.org/uniprot/Q16595>
wdt:P31 protein
wdt:P3417 "Frataxin"
wdt:P352 "Q16595"
wdt:P361 Frataxin
Frataxin/CyaY superfamily
Putative uncharacterized transport proteins
Frataxin conserved site, protein family
wdt:P373 "Frataxin"
wdt:P527 Frataxin conserved site
wdt:P591 "1.16.3.1"
wdt:P6366 "2779314966"
wdt:P637 "NP_000135"
"NP_852090"
wdt:P638 "1EKG"
"1LY7"
"3S4M"
"3S5D"
"3S5E"
"3S5F"
"3T3J"
"3T3K"
"3T3L"
"3T3T"
"3T3X"
wdt:P646 "/m/027lc45"
wdt:P680 metal ion binding
oxidoreductase activity
ferric iron binding
ferrous iron binding
ferroxidase activity
2 iron, 2 sulfur cluster binding
iron chaperone activity
protein binding
wdt:P681 cytosol
L-cysteine desulfurase complex
mitochondrial matrix
mitochondrion
cytoplasm
wdt:P682 proprioception
small molecule metabolic process
negative regulation of apoptotic process
positive regulation of cell population proliferation
positive regulation of cell growth
embryo development ending in birth or egg hatching
negative regulation of release of cytochrome c from mitochondria
cellular iron ion homeostasis
ion transport
iron ion homeostasis
negative regulation of organ growth
protein autoprocessing
response to iron ion
positive regulation of catalytic activity
adult walking behavior
cellular response to hydrogen peroxide
mitochondrion organization
heme biosynthetic process
regulation of ferrochelatase activity
iron incorporation into metallo-sulfur cluster
negative regulation of multicellular organism growth
positive regulation of lyase activity
iron-sulfur cluster assembly
aerobic dissimilation
positive regulation of succinate dehydrogenase activity
positive regulation of aconitate hydratase activity
oxidative phosphorylation
wdt:P692 <http://commons.wikimedia.org/wiki/Special:FilePath/PBB%20GE%20FXN%20205565%20s%20at%20fs.png>
wdt:P702 FXN
wdt:P703 human beings
wdt:P705 "ENSP00000366482"
"ENSP00000379650"
"ENSP00000379652"
"ENSP00000418015"
"ENSP00000419243"
"ENSP00000495217"
wdt:P7260 "9.B.21.1.1"
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