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rdfs:label
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"Doença desmoide"@pt
"Doença desmoide"@pt-br
"desmoid disease, hereditary"@en
"tumeur desmoïde héréditaire"@fr
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|
skos:altLabel
|
"Aggressive fibromatosis"@en
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|
"DESMOID DISEASE, HEREDITARY"@en
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|
"Deep Fibromatosis"@en
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"Deep Fibromatosis/Desmoid Tumor"@en
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"Desmoid Fibromatosis"@en
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|
"Desmoid Tumor Caused by Somatic Mutation"@en
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|
"Desmoid type fibromatosis"@en
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|
"Desmoid-Type Fibromatosis"@en
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|
"Fibromatosis, Familial Infiltrative"@en
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|
"desmoid tumor"@en
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"hereditary desmoid disease"@en
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schema:description
|
"desmoid tumor (DT) is a benign, locally invasive soft tissue tumor associated with a high recurrence rate but with no metastatic potential"@en
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|
schema:dateModified
|
"2026-10-24T00:40:15+00:00"^^xsd:dateTime
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schema:version
|
2560167837
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wikibase:identifiers
|
10
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|
12
|
|
wikibase:sitelinks
|
0
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wikibase:statements
|
37
|
|
p:P11430
|
wd:statement/Q55950219-18c2dcb6-4b9c-1b2c-348a-0e05ec29c32f
|
|
p:P11956
|
wd:statement/Q55950219-619C20D3-5DD2-4306-AEB8-BAC2D33CA003
|
|
p:P14914
|
wd:statement/Q55950219-9AEC470F-D52F-4F92-9EEB-C3D1A1E2C9E0
|
|
p:P1550
|
wd:statement/Q55950219-574057B7-6A54-4DCA-89BA-2E58F98B3FAE
|
|
p:P1748
|
wd:statement/Q55950219-3485A680-8C9D-4D44-B230-F3D9239FFCBC
|
|
p:P2176
|
wd:statement/Q55950219-7C26B394-B746-46A3-832D-C8B7915977D4
|
|
p:P2293
|
wd:statement/Q55950219-CB53017A-A4F3-47C7-919F-5D0F62F4C9E8
|
|
wd:statement/Q55950219-ECBC4C8E-C782-4D96-986D-2F55F5503C65
|
|
p:P279
|
wd:statement/Q55950219-4f05d065-444b-b7f0-432d-1f150755fd15
|
|
wd:statement/Q55950219-75572CA3-269D-48E0-ABB4-731B1F36F895
|
|
wd:statement/Q55950219-B12F16BB-567C-42DC-BB70-FC1A86483E09
|
|
p:P2841
|
wd:statement/Q55950219-0889F5D7-BCE4-467A-AB3A-091A6F78125D
|
|
wd:statement/Q55950219-67B52A8B-3FDD-4B4C-9030-2E0E09BABAD5
|
|
p:P2888
|
wd:statement/Q55950219-77D83B5B-C090-4EA7-B7C5-B3E2C684F30D
|
|
wd:statement/Q55950219-C5EF3917-2029-49C3-8FD9-209089B97989
|
|
wd:statement/Q55950219-D71BF8B7-669E-4C6F-97F5-D69997CADF09
|
|
p:P2892
|
wd:statement/Q55950219-23F89A00-3437-4CF0-A44A-BE6F1888E84B
|
|
wd:statement/Q55950219-F17E446A-1D5A-4C40-BDD1-D7BD067DE512
|
|
wd:statement/Q55950219-F1F97FAE-78F9-4B3F-8B44-662ED653340C
|
|
p:P31
|
wd:statement/Q55950219-42210B16-F875-4239-BE31-02B8C087EE07
|
|
p:P4229
|
wd:statement/Q55950219-41DE660B-AFA6-4113-A9F3-8A8FEC1E2C00
|
|
p:P492
|
wd:statement/Q55950219-6380CD25-687D-48CE-BA2F-A18B412B4187
|
|
p:P5270
|
wd:statement/Q55950219-4E1E0224-2D0C-4393-8148-F1D4F11C2590
|
|
p:P6532
|
wd:statement/Q55950219-09B50FAA-0AEB-4B0D-A8F4-5F1C27620D48
|
|
wd:statement/Q55950219-2B642562-6FBE-46D8-A0E4-ED1B7C33912C
|
|
wd:statement/Q55950219-2FDF42D6-E642-4410-B0FF-3351761284B8
|
|
wd:statement/Q55950219-58B6136D-2D80-417F-89EE-88B706C3BAE3
|
|
wd:statement/Q55950219-8E7C5256-21C8-41A1-B5C7-25D990A1C305
|
|
wd:statement/Q55950219-953CD595-2144-43A7-86CC-D9D19B9079CC
|
|
wd:statement/Q55950219-9F9059BC-528C-4BA5-9B8E-0E00D2B4486D
|
|
wd:statement/Q55950219-A2DE77C3-C2CF-42C5-BABF-591AA0BBB36E
|
|
wd:statement/Q55950219-A9EDAC50-91C5-4781-8D4C-BCAC7BFE98E1
|
|
wd:statement/Q55950219-CA38C023-794B-4C7F-A472-0F392F5AA3AE
|
|
wd:statement/Q55950219-D775C71A-3D6B-4554-8E7F-6E7486BCD503
|
|
wd:statement/Q55950219-EACCD891-31B1-4743-9B21-8D3B443F49E3
|
|
wd:statement/Q55950219-F014D5D4-70C9-47DD-AB51-FCBFBADEE161
|
|
p:P699
|
wd:statement/Q55950219-8BB713FC-0B10-400E-8837-42F6885C6082
|
|
p:direct-normalized/P5270
|
<http://purl.obolibrary.org/obo/MONDO_0007608>
|
|
p:direct-normalized/P699
|
<http://purl.obolibrary.org/obo/DOID_DOID:0111349>
|
|
wdt:P11430
|
"DI-01711"
|
|
wdt:P11956
|
"0009907"
|
|
wdt:P14914
|
"D00873"
|
|
wdt:P1550
|
"873"
|
|
wdt:P1748
|
"C9182"
|
|
wdt:P2176
|
meloxicam
|
|
wdt:P2293
|
APC
|
|
CTNNB1
|
|
wdt:P279
|
syndrome
|
|
autosomal genetic disease
|
|
aggressive fibromatosis
|
|
wdt:P2841
|
juvenile onset
|
|
adult onset
|
|
wdt:P2888
|
<http://identifiers.org/doid/DOID:0111349>
|
|
<http://purl.obolibrary.org/obo/DOID_0111349>
|
|
<http://www.orpha.net/ORDO/Orphanet_873>
|
|
wdt:P2892
|
"C0079218"
|
|
"C1851124"
|
|
"C2675440"
|
|
wdt:P31
|
type of disease
|
|
wdt:P4229
|
"D48.1"
|
|
wdt:P492
|
"135290"
|
|
wdt:P5270
|
"MONDO_0007608"
|
|
wdt:P6532
|
Abnormal abdominal wall morphology
|
|
Cronkhite-Canada syndrome
|
|
malabsorption
|
|
gastrointestinal bleeding
|
|
bowel obstruction
|
|
sepsis
|
|
abdominal pain
|
|
osteolysis
|
|
fibroma
|
|
myalgia
|
|
arthralgia
|
|
chest pain
|
|
hydronephrosis
|
|
wdt:P699
|
"DOID:0111349"
|